2991: cataract surgery in keratoglobus (Ehlers Danlos Syndrome)

2991: cataract surgery in keratoglobus (Ehlers Danlos Syndrome)

Close-up view of an eye undergoing cataract surgery, highlighting challenges related to keratoglobus, including weak cornea and irregular iris. Text mentions the patient has Ehlers Danlos Syndrome and identifies the operating surgeon.

In this extraordinary case, our guest surgeon tackles cataract surgery in a patient presenting with keratoglobus and comorbid Ehlers Danlos syndrome. This rare combination introduces many complex surgical challenges, including a structurally weak cornea, significant zonulopathy, and an irregular iris. The diffuse corneal thinning makes clear corneal incision architecture highly volatile, requiring meticulous wound construction and closure to avoid ectasia or leaks. Simultaneously, the systemic collagen defect manifests intraocularly as significant zonular laxity, demanding modified nuclear division techniques and the proactive use of capsular stabilization devices. Watch how the surgeon carefully maneuvers through each step of this unique case to ensure stable intraocular lens centration without compromising the fragile ocular tissue. What specific adjustments do you make to your incision and phaco parameters when operating on an ultra thin or ectatic cornea? Please comment your thoughts and management strategies below.

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